All Relations between Hearing Loss and Deafness

Publication Sentence Publish Date Extraction Date Species
Ch Kuhlmann, W Scheidemann, M Bachmann, G F Schusse. [Brainstem auditory evoked responses in horses with hearing loss and during general anesthesia]. Schweizer Archiv fur Tierheilkunde. vol 166. issue 7. 2024-07-08. PMID:38975650. horses with right sided external otitis: right moderate to severe conductive hearing loss (significantly prolonged latencies of i, iii, v and interpeak latencies i-iii, i-v, iii-v; thresholds of hearing levels 60 to 80 db right); horses with left sided external otitis: left severe conductive hearing loss (no correct identification of baer peaks, latencies not measurable, 80 db); horse with left sided head trauma: severe left sided conductive hearing loss (blood in the left external ear canal, no visible tympanic membrane, no correct identification of baer peaks, latencies not measurable, 80 db); horses with head shaking: mild sensorineural hearing loss on both sides (on both sides osseous parts ii/iii with keratin scales of the junction, visible tympanic membranes, significantly prolonged v, i-iii, i-v, 40 db); moderate to severe skittish horses with chronic eye disease (mostly left sided equine recurrent uveitis): moderate sensorineural hearing loss on both sides (normal otoscopical findings, significantly prolonged latencies and interpeak latencies left; i-v, iii-v right, 60 db, pathological involvement in the auditory pathway of the brainstem between the cochlear nucleus and colliculus caudalis); horse with a tinnitus on both sides: mild sensorineural hearing loss on both sides (normal otoscopical findings, prolonged v, i-iii, i-v, iii-v, 40 db, pathology of auditory nerve, cochlear nucleus and above the level of this nucleus); american paint horses: sensorineurale deafness on both sides (normal otoscopical findings, absent baer peaks, isoelectric lines and 80 db on both sides). 2024-07-08 2024-07-11 Not clear
T Stöver, S K Plontke, W K Lai, T Zahnert, O Guntinas-Lichius, H-J Welkoborsky, A Aschendorff, T Deitmer, A Loth, S Lang, S Dazer. The German cochlear implant registry: one year experience and first results on demographic data. European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery. 2024-07-08. PMID:38977469. this is particularly true when providing patients with severe hearing loss or deafness with a cochlear implant (ci). 2024-07-08 2024-07-12 Not clear
Badriah G Alasmari, Mohammed Alpakra, Sara S Hassanien, Abdelhakam A Elmugadam, Lina Elzubair, Enaam A Suliman, Somayah A Alghubish. A Novel Variant in the DIAPH1 Gene Causing Macrothrombocytopenia and Non-syndromic Hearing Loss in a Pediatric Saudi Girl. Cureus. vol 16. issue 5. 2024-06-25. PMID:38915998. dominant gain-of-function diaph1 variants cause macrothrombocytopenia and sensorineural deafness (autosomal dominant non-syndromic hearing loss 1 (dfna1)), while homozygous loss of diaph1 results in seizures, cortical blindness, and microcephaly syndrome (scbms). 2024-06-25 2024-06-27 Not clear
Jean Defourn. TBC1D24 is likely to regulate vesicle trafficking in glia-like non-sensory epithelial cells of the cochlea. The International journal of developmental biology. 2024-06-13. PMID:38869222. mutations in the gene encoding tre2/bub2/cdc16 (tbc)1 domain family member 24 (tbc1d24) protein are associated with a variety of neurological disorders, ranging from non-syndromic hearing loss to drug-resistant lethal epileptic encephalopathy and doors syndrome [deafness, onychodystrophy, osteodystrophy, intellectual disability (formerly referred to as mental retardation), and seizures]. 2024-06-13 2024-06-15 mouse
María Aragonés Redó, Ignacio Pla Gil, Tomàs Pérez-Carbonell, Clara Espina González, Antonio Morant Ventura, Jaime Marco Algarr. Prospective study of location in patients with unilateral and asymmetric hearing treated with cochlear implant. Acta otorrinolaringologica espanola. 2024-05-26. PMID:38797372. however, this ability is compromised in patients with single-sided deafness (ssd) and asymmetric hearing loss (ahl), negatively impacting their daily functioning. 2024-05-26 2024-05-31 Not clear
María Aragonés Redó, Ignacio Pla Gil, Tomàs Pérez-Carbonell, Clara Espina González, Antonio Morant Ventura, Jaime Marco Algarr. Prospective study of location in patients with unilateral and asymmetric hearing treated with cochlear implant. Acta otorrinolaringologica espanola. 2024-05-26. PMID:38797372. the main objective of the study was to quantify the degree of sound source localization in patients with single-sided deafness or asymmetric hearing loss using a cochlear implant (ci) and to compare between the two subgroups. 2024-05-26 2024-05-31 Not clear
Lina Pan, Chunrui Li, Lanxia Meng, Guoxin Zhang, Li Zou, Ye Tian, Sen Chen, Yu Sun, Dandan Su, Xingyu Zhang, Min Xiong, Tingting Xiao, Danhao Xia, Zhengyuan Hong, Zhentao Zhan. GDF1 ameliorates cognitive impairment induced by hearing loss. Nature aging. 2024-03-16. PMID:38491289. knockdown of gdf1 mimics the detrimental effect of hearing loss on cognition, while overexpression of gdf1 in the hippocampus attenuates the cognitive impairment induced by deafness. 2024-03-16 2024-03-19 mouse
Emma Hershey, Lisa Chionis, Ruby Kazemi, Carla Valenzuela, Hussam K El-Kashlan, Gregory J Basura, Emily Z Stucke. Changing Management of Intravestibular Schwannomas in the Era of Cochlear Implantation for Single-Sided Deafness. Otology & neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology. 2024-02-16. PMID:38361345. patients with ils confined to the semicircular canals and the vestibule (intravestibular schwannomas) are potential candidates for cochlear implantation for hearing rehabilitation, a new option for patients with unilateral hearing loss since the 2019 fda approval of cochlear implant (ci) for single-sided deafness. 2024-02-16 2024-02-18 Not clear
Yue Qiu, Le Xie, Xiaohui Wang, Kai Xu, Xue Bai, Sen Chen, Yu Su. Abnormal Innervation, Demyelination, and Degeneration of Spiral Ganglion Neurons as Well as Disruption of Heminodes are Involved in the Onset of Deafness in Cx26 Null Mice. Neuroscience bulletin. 2024-02-04. PMID:38311706. the cx26-cko mice showed severe hearing loss and massive loss of hair cells and deiter's cells, which represented the extreme form of human deafness caused by gjb2 gene mutations. 2024-02-04 2024-02-07 mouse
Lang Zhang, Jin-Yuan Yang, Qiu-Quan Wang, Xue Gao, Guo-Jian Wang, Ming-Yu Han, Dong-Yang Kang, Dong-Yi Han, Sha-Sha Huang, Yong-Yi Yua. MPZL2-a common autosomal recessive deafness gene related to moderate sensorineural hearing loss in the Chinese population. BMC medical genomics. vol 17. issue 1. 2024-01-23. PMID:38254107. mutations in mpzl2, the characteristic genetic etiology of autosomal recessive deafness loci 111 (dfnb111), cause non-syndromic and moderate sensorineural hearing loss. 2024-01-23 2024-01-25 Not clear
Jack J Wazen, Christine S Kim, Carmelo Ortega, Tonya King, Seth R Schwartz, Daniel M Zeitle. Benefits of unilateral cochlear implantation in adults with asymmetric hearing loss: Audiologic and patient-related outcome measures. American journal of otolaryngology. vol 45. issue 2. 2023-12-15. PMID:38101137. to investigate the benefits of cochlear implantation in adults with single-sided deafness (ssd) and asymmetric hearing loss (ahl). 2023-12-15 2023-12-18 Not clear
Iva Speck, Elisabeth Gundlach, Sandra Schmidt, Nadine Spyckermann, Anke Lesinski-Schiedat, Ann-Kathrin Rauch, Antje Aschendorff, Kruthika Thangavelu, Katrin Reimann, Susan Arnd. Auditory capacity of the better-hearing ear in asymmetric hearing loss. European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery. 2023-11-25. PMID:38006462. our aim was to investigate the course of the hearing capacity of the better-hearing ear in single-sided deafness (ssd) and asymmetric hearing loss (ahl) over time, in a multicenter study. 2023-11-25 2023-11-28 Not clear
Jiang Li, Byung Yoon Choi, Yasmin Eltawil, Noura Ismail Mohamad, Yesai Park, Ian R Matthews, Jin-Hee Han, Bong Jik Kim, Elliott H Sherr, Dylan K Cha. TMTC4 is a hair-cell-specific human deafness gene. JCI insight. 2023-11-09. PMID:37943620. these findings provide evidence that tmtc4 is a deafness gene in humans and further implicate the upr in progressive hearing loss. 2023-11-09 2023-11-20 mouse
Yingting Qi, Ke Zhan. [Intervention effects of bone conduction hearing aids in patients with single-sided deafness and asymmetric hearing loss]. Lin chuang er bi yan hou tou jing wai ke za zhi = Journal of clinical otorhinolaryngology, head, and neck surgery. vol 37. issue 11. 2023-10-31. PMID:37905490. [intervention effects of bone conduction hearing aids in patients with single-sided deafness and asymmetric hearing loss]. 2023-10-31 2023-11-08 Not clear
Luis Lassaletta, Miryam Calvino, Isabel Sanchez-Cuadrado, Piotr Henryk Skarzynski, Katarzyna B Cywka, Natalia Czajka, Justyna Kutyba, Dayse Tavora-Vieira, Paul Van de Heyning, Griet Mertens, Hinrich Staecker, Bryan Humphrey, Mario Zernotti, Maximo Zernotti, Astrid Magele, Marlene Ploder, Julia Speranza Zabe. QoL, CIs, QALYs, and Individualized Rehabilitation: The Clinical and Practical Benefits of Regularly Assessing the Quality of Life of Adult Cochlear Implant Recipients. International journal of environmental research and public health. vol 20. issue 20. 2023-10-27. PMID:37887644. participants (n = 101) were unilateral ci users with single-sided deafness (ssd; n = 17), asymmetrical hearing loss (ahl; n = 26), or bilateral hearing loss (uni; n = 58). 2023-10-27 2023-11-08 human
Jingliang Cheng, Ting Li, Qi Tan, Jiewen Fu, Lianmei Zhang, Luquan Yang, Baixu Zhou, Lisha Yang, Shangyi Fu, Alora Grace Linehan, Junjiang F. Novel, pathogenic insertion variant of GSDME associates with autosomal dominant hearing loss in a large Chinese pedigree. Journal of cellular and molecular medicine. 2023-10-21. PMID:37864300. nonsyndromic hearing loss (nshl) is a genetically diverse, highly heterogeneous condition characterised by deafness, and gasdermin e (gsdme) variants have been identified as directly inducing autosomal dominant nshl. 2023-10-21 2023-11-08 human
Jingliang Cheng, Ting Li, Qi Tan, Jiewen Fu, Lianmei Zhang, Luquan Yang, Baixu Zhou, Lisha Yang, Shangyi Fu, Alora Grace Linehan, Junjiang F. Novel, pathogenic insertion variant of GSDME associates with autosomal dominant hearing loss in a large Chinese pedigree. Journal of cellular and molecular medicine. 2023-10-21. PMID:37864300. while many nshl cases associated with gsdme involve the skipping of exon 8, there is another, less understood pathogenic insertion variant specifically found in chinese pedigrees that causes deafness, known as autosomal dominant 5 (dfna5) hearing loss. 2023-10-21 2023-11-08 human
Jingliang Cheng, Ting Li, Qi Tan, Jiewen Fu, Lianmei Zhang, Luquan Yang, Baixu Zhou, Lisha Yang, Shangyi Fu, Alora Grace Linehan, Junjiang F. Novel, pathogenic insertion variant of GSDME associates with autosomal dominant hearing loss in a large Chinese pedigree. Journal of cellular and molecular medicine. 2023-10-21. PMID:37864300. in conclusion, we have successfully identified a novel pathogenic insertion variant of gsdme in a chinese pedigree that causes deafness, shedding light on the genetic basis of hearing loss within this specific family. 2023-10-21 2023-11-08 human
Jingliang Cheng, Ting Li, Qi Tan, Jiewen Fu, Lianmei Zhang, Luquan Yang, Baixu Zhou, Lisha Yang, Shangyi Fu, Alora Grace Linehan, Junjiang F. Novel, pathogenic insertion variant of GSDME associates with autosomal dominant hearing loss in a large Chinese pedigree. Journal of cellular and molecular medicine. 2023-10-21. PMID:37864300. our findings expand the spectrum of known variants associated with gsdme-related deafness and may further support both the underlying gain-of-function mechanism and functional associations of gsdme hearing loss variants. 2023-10-21 2023-11-08 human
Heidi Olze, Jana Vater, Moritz Gröschel, Agnieszka J Szczepe. [Cochlear implant and tinnitus]. HNO. 2023-10-10. PMID:37815555. current ci indications include bilateral (double-sided) profound hearing loss and deafness (dsd), unilateral (single-sided) deafness (ssd), and asymmetric hearing loss (ahl). 2023-10-10 2023-10-15 Not clear